ABSTRACT
Gonadotropin independent precocious puberty due to recurrent ovarian cysts evokes a Mc-Cune Albright syndrome (MAS). This syndrome is characterized by endocrine dysfunctions such as precocious puberty, polyostotic fibrous dyplasia and cafe au lait skin lesions. Here we want to report a 3.9 years-old girl with gonadotropin independent precocious puberty and cafe au lait spots suggesting MAS. Her skeletal X- rays were normal. Fibrous dyplasia of the bones were detected only in the bone scintigraphy. We want to emphasize the importance of bone scintigraphy to detect fibrous dysplasia.